DBT Rabbit mAb - A25001
Nur noch %1 verfügbar
Catalog #
AB-A25001
Ab
135,00 €
The branched-chain alpha-keto acid dehydrogenase complex (BCKD) is an inner-mitochondrial enzyme complex involved in the breakdown of the branched-chain amino acids isoleucine, leucine, and valine. The BCKD complex is thought to be composed of a core of 24 transacylase (E2) subunits, and associated decarboxylase (E1), dehydrogenase (E3), and regulatory subunits. This gene encodes the transacylase (E2) subunit. Mutations in this gene result in maple syrup urine disease, type 2. Alternatively spliced transcript variants have been described, but their biological validity has not been determined.
| Isotype | IgG |
|---|---|
| Datasheet URL | https://abclonal.com/instructions/pdf/A25001 |
| Alternative Names | E2; E2B; BCATE2; BCKADE2; BCKAD-E2; BCKDH-E2; BCOADC-E2; [KD Validated] DBT |
| Species | Human |
| Source | Rabbit |
| Purity | Affinity purification |
| Immunogen | Recombinant fusion protein containing a sequence corresponding to amino acids 62-247 of DBT (NP_001909.4). |
| Storage | Store at -20℃. Avoid freeze / thaw cycles.|Buffer: PBS with 0.05% proclin300,0.05% BSA,50% glycerol,pH7.3. |
| Conjugate | Unconjugated |